CRETINISM.

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This singular disorder was first discovered and noticed by Plater, about the middle of the seventeenth century, among the poor inhabitants of Carinthia and the Valais, where, as in the valleys of the Lower Alps and the Pyrenees, it is also found to be an endemic affection. According to Sir George Staunton, it is also observed in Chinese Tartary. It has been erroneously confounded by some writers with bronchocele and rachitis, from both of which it is totally distinct.

Cretinism presents various modifications in kind, and every intermediate grade between that extreme degree of physical and mental debasement which is characterized by the utmost deformity, and entire absence of mental manifestation, the organic and vegetative functions only being performed. There are certain circumstances that distinguish cretins from idiots; and their infirmities appear to depend upon endemic or local causes, regarding which much diversity of opinion has prevailed both amongst medical men and travellers.

The cretins were also called Cagots and Capots. In Navarre these unfortunates go by the name of Gaffos and Ganets; and in various valleys of the Pyrenees they are called GÉzits or Gezitains. Near La Rochelle, some of them are also found, and there they are known by the appellation of Coliberts; and in Britanny Cacons and Cagneux. The derivation of these names shows the contempt and disgust that they excited,—Cagot, according to Scaliger, being derived from Canis Gottus, or Dog of a Goth; Colibert is traced to quasi libertus, or slave. The Spaniards call them Gavachos, a term of reproach, which they also applied to the French during the Peninsular struggle.

The body of these poor creatures is stunted, their height not exceeding four feet. There is a total want of due proportion between it and the other parts, the height of the head with reference to the body being from one-fourth to one-fifth, instead of one-eighth, the natural proportion; the neck is strong, and bent downwards; the upper limbs reach below the knees, and the arm is shorter than the fore-arm; the chest narrow, the abdomen hemispherical, and of a length not exceeding the height of the head; the thighs, with the haunches, of greater width than the shoulders, and shorter than the legs, the calves of which are wanting; the feet and toes distorted. In the head, the masticating organs, the lower jaw, and the nose, preponderate considerably over the organs of sense and intelligence; the skull is depressed, and forms a lengthened and angular ellipsis; the receding forehead presents internally large frontal sinuses, to which the brain has yielded part of its place; the top of the head is flattened, instead of being vaulted; the occiput projects but slightly, and runs almost even with the nape of the neck, as in ruminating animals. The face is neither oval nor round, but spread out in width; the eyes are far apart, slightly diverging, small, and deep-seated in their orbits; the pupil contracted, and not very sensitive to light; the eyelids, except when morbidly swollen, are flaccid and pendent. Their look is an unmeaning stare, and turns with indifference from every thing that is not eatable. The elongated form of the lower jaw, the thick and puffed lips, give them a greater resemblance to ruminating creatures than to man. The tongue is rather cylindrical than flat, and the saliva is constantly running from the angles of their mouth. Enlargement of the thyroid glands generally prevails, sometimes to an enormous extent. Indeed, this appearance is commonly considered as a distinguishing sign of cretinism. The other glands of the throat are also obstructed. Many of these poor wretches are both deaf and dumb; yet do they appear unconscious of their miserable existence. Stretched out or gathered up under the solar rays, their head drooping in idiotic apathy, they are only roused from their torpor when food is presented to them.

This endemic malady is supposed to arise from the use of snow-water, or of water impregnated with calcareous earth. Both of these opinions are without foundation. All the inhabitants of districts near the glaciers, drink snow and ice waters without being subject to the disorder; and the common waters of Switzerland, strongly impregnated with calcareous substances, are most salubrious. At Berne, the waters are extremely pure, yet Haller observed that swellings of the throat are not uncommon. De Saussure has assigned another cause, and refers the disorder to the physical features of the mountainous districts in which it prevails. The valleys, he tells us, are surrounded with very high mountains, sheltered from currents of fresh air, and exposed to the direct, and what is worse, the reflected rays of the sun. They are marshy, and hence the atmosphere is humid, close, and oppressive. When to these chorographical causes, he further says, we add the domestic ones, which are also well known to prevail among the poor of these regions,—such as innutritious food, indolence, and uncleanliness, with a predisposition to the disease from an hereditary taint of many generations,—we can sufficiently account for the prevalence of cretinism in such places, and for the most humiliating characters it is ever found to assume.

This specious reasoning, however, is overthrown by observation. In the first instance, this character of the country does not affect its other inhabitants; and secondly, the goÎtre is found in warm latitudes, and Mungo Park observed it amongst the Africans of Bambara, on the banks of the Niger. Marsden has also seen it at Sumatra. Moreover, this affection is scarcely ever seen in the mountains, but principally prevails in the valleys.

It is more than probable that these ill-favoured creatures belong to a particular race; for we must take care not to confound goÎtre with cretinism, since goÎtre is common where cretinism is prevalent. It has been remarked that the offspring of the natives of the Valais who intermarry with persons from the Italian side of the Alps, are more subject to goÎtres than those born of native parents; and that females who have husbands from the higher Alps, seldom have children affected with this infirmity. It is pretty clear that in these observations, goÎtre and cretinism are confounded.

That these miserable cagots belong to a particular race of men, most probably accidentally degraded in their transmission from our primitive stock, appears most likely. We have sought the derivation of the several terms of contempt and disgust attached to them in different countries, to which migration may have led their parents. Some writers have traced their descent to the Goths and Vandals, thus chastised for their devastations. GÉbelin, BelleforÊt, and Ramont consider them as descendants of the Visigoths; while Marca, bishop of CousÉrans, denounces them at once as Jews and Saracens; and other clerical writers have maintained that they are the miserable relicts of the heretic Albigenses who had escaped the holy massacres of 1215; although there did exist cagots in the year 1000, in the abbey of St. Luc, as they are described in a for of Navarre, bearing date 1074, and issued by Ramirez.

These helpless beings have also been considered as the offspring of Bohemians and gipsies. Bishop, or rather Senator Gregoire, maintained that they sprung from the hordes of northern barbarians who overran the south of Europe in the third and fourth centuries. Whatever might have been the origin of these poor creatures, they seem to share that ignominious destiny that has marked various races in different countries. The Agotos of Navarre, the Maragotos of Leon, the Batuecos of Castile, the Wendes of Silesia, are all held in as much contempt as the Parias and the Vaddahs of India. Even in Otaheite a degraded caste was found, from which victims were selected to appease Divine wrath, or propitiate their gods.

The traditional contempt in which certain races are held, a contempt that seems to have affected their physical appearance, may perhaps be traced to the degradation of slavery, that seems to deprive man of all his proud attributes, both in a moral and physical point of view. The effects of tyranny, and the distinctions that oppression has created in the several castes and ranks of mankind, are every where evident. What a difference exists in Scotland between the chieftains and the humbler individuals of their clans!—between the naÏres of India and their vassals! In France, said Buffon, you may distinguish by their aspect, not only the nobility from the peasantry, but the superior order of nobility from the inferior, these from the citizens, and citizens from the peasants. “The field-slaves in America,” observes the enlightened Dr. Smith, “are badly clothed, fed, and lodged, live in small huts in the plantations, remote from the example and society of their superiors. Living by themselves they retain many of the customs and the manners of their ancestors. The domestic servants, on the other hand, who are kept near the persons or employed in the families of their masters, are treated with great lenity, their service is light, they are well fed and clothed. The field-slaves, in consequence of their condition, are slow in changing the aspect and figure of Africa; while the domestic servants have advanced far before them in acquiring the agreeable and regular features, and the expressive countenance, of civilized society. The former are frequently ill-shaped; they preserve in a great degree the African lips, and nose, and hair; their genius is dull, and their countenances sleepy and stupid. The latter are straight and well proportioned; their hair extends to three or four, sometimes even to six or eight inches; the size of their mouth is handsome, their features regular, their capacity good, and their looks animated.” Dr. Prichard has also stated that similar changes become visible in the third and fourth generations in the West India islands; and I have seen several negresses in those colonies perfectly beautiful. In the Bahama islands I knew a female slave of the name of Leah, belonging to my late friend Mr. Commissary Brookes, as black as jet, and descended in the third generation from African parents, whose features would have vied in symmetry with the fairest specimen of the Caucasian race.

Let us not, therefore, seek in snow-water or calcareous impregnations for the causes of deformity and degradation in any unfortunate castes of mankind. Their misery may more probably be traced to the iron rod of despotism, or the oppression of bigotry,—influences that mark out races as abject slaves, or objects of Divine wrath, that ought to be scorned by the wealthy and the powerful, and spurned and persecuted by the faithful and the elect; although, when it has served its purposes, priestcraft has held up the cagot, and the leper, and the idiot, as objects of veneration. When the tourist, in his Alpine and Pyrenean excursions, meets a wretched cagot, let him pause and contemplate the offspring of slavery, and reflect on what man is, and on what man might be,—nay, on what man will be.


                                                                                                                                                                                                                                                                                                           

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